HISTORY
Female patient , 33 yo, presented by severe heart failure for 1 year, previous diagnosis : dilated cardiomyopathy . Decreased S1. audible S3, 2/6 apical systolic murmur. She was sent to MEDIC for cardiac MSCT to rule out Coronary artery disease.
EKG
Short PR, delta waves, QS in V2-V6, D1 aVL
ECHOCARDIO+ TDI and 3 D Echocardiography
Decreased LV systolic function , LV diastolic dysfunction , LV diastolic dysfunction
Prominent trabeculae, spongiformed LV , Diagnostic criteria NC/C leyer > 2
Noncompacted cardiomyopathy Echocardiography: Apical 4 C view and Parasternal short axis view
Prominent trabeculations and spongiformed myocardium of LV
MS CT 640
Intertrabecular Recesses, Multiple Trabeculae , Predominant location at Apex, mid lateral, mid inferior . NC layer/ C layer > 2,2, Involving >2 segments, Sens. 100%, Spec. 95% (Tomography, volume 6, Issue 5, Sept.-Oct. 2012, pp 346-354)
MSCT 640: 3D Imaging =Trabeculated and spongiformed LV
Video clip from apex view
Summary
Reported by Engberding and Benber in 1984 :Mutation in LDB3, genetic cardiomyopathy
Myocardial sinusoids
Severe heart failure, arrhythmias, thrombus formation, sudden death
Diagnosis by Echocardiography, MRI, MSCT
Medical treatment ( ACEI, Betabloker, Aspirin, Anticoagulant ), ICD, heart transplant.
Long term prognosis is unknown
Value of cardiac MSCT in patient with heart failure.